Epignathus of a fetus is a rare type of oropharyngeal teratoma rarely reported in the literature, especially from the Indian subcontinent. Antenatal diagnosis of this condition is even rarer. The overall survival rates with these lesions have been between 17 and 87.5%. However, survival in the setting of antenatally diagnosed teratomas has only been described anecdotally. Transposition of the great arteries (TGA) is an isolated abnormality in about 90% of the cases and rarely is associated with extracardiac malformation. Gallbladder duplication resulting in two separate gallbladders is a rare congenital anomaly. We present an unusual case of antenatally diagnosed massive oropharyngeal teratoma, which was associated with transposition of great arteries and duplicated gallbladder. To conclude, the antenatal diagnosis of TGA decides the postnatal outcomes and hence requires planned delivery and further management. A combination of these conditions may cause airway obstruction and respiratory compromise, like in our case, which necessitated termination of pregnancy.
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