Citation Information :
Begic N, Begic Z, Iglica A, Begic E, Dekovic S, Suljevic A, Jonuzovic-Prosic S. A Single Ventricle Defect: A Case Report from Fetal Echocardiography to Cardiac Surgery. Donald School J Ultrasound Obstet Gynecol 2022; 16 (1):91-94.
Objective: The aim of the paper is to show a report of rare, life-threatening congenital heart defect (CHD), emphasizing the importance of fetal echocardiography for the diagnosis and treatment of CHD improving the outcome.
Case description: The diagnosis of the single ventricle, rudimentary left ventricle, common atrium, double outlet right ventricle (DORV), transposition of the great arteries (TGA), and mild pulmonary stenosis was made prenatally at routine fetal echocardiography scan and confirmed postnatally by pediatric cardiologist assessment, who indicated postnatal cardiosurgical treatment. According to planned treatment, the first step was establishment of the central shunt (polytetrafluoroethylene 3.5 mm) between the ascending aorta and the left pulmonary artery (LPA), followed by a bidirectional Glenn shunt. The patient was hemodynamically stable at discharge, treated with acetylsalicylic acid as antiaggregating agent. In the future, Fontan procedure as the third surgical procedure is planned.
Conclusion: Accurate prenatal diagnosis of CHD confirmed postnatally enabled to prepare medical team and parents for the treatment enabling survival of the infant and better parental coping with the diagnosis and treatment of severe life-threatening CHD.
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